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Rare diseases 



In the database for rare diseases of the Swedish National Board of Health and Welfare you can find information about diseases or disorders which affect fewer than 100 people per million, and which lead to a marked degree of disability.

 


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Diagnosis Synonyms
13q deletion syndrome Monosomy 13q syndrome
1p36 deletion syndrome Monosomy 1p36
22q11 deletion syndrome DiGeorge syndrome, Velo-cardio-facial syndrome, CATCH 22
5p deletion syndrome  
AB variant of GM2 gangliosidosis  
Acid maltase deficiency  
Acquired epilectic aphasia  
Acrocephalosyndactyly type 1  
Activator protein deficiency  
Acute intermittent porphyria AIP
AGU  
AIP  
AIS  
Alagille syndrome Arteriohepatic dysplasia
Albers-Schönberg disease  
Alpha-galactosidase A deficiency  
Alport syndrome --
ALPS  
ALS  
Alström syndrome Alström-Hallgren syndrome
Alström-Hallgren syndrome  
Amyotrophic lateral sclerosis ALS, Progressive spinal muscular atrophy, Progressive bulbar palsy, Pseudobulbar palsy, Primary...
Anderson-Fabry disease  
Androgen insensitivity syndrome AIS, Androgen resistance syndrome, Testicular feminisation syndrome
Androgen resistance syndrome  
Angelman syndrome --
Angiokeratoma corporis diffusum  
Angioosteohypertrophy syndrome  
Anhidrotic ectodermal dysplasia  
Anonymous Brain disease of unknown cause
Apert syndrome Acrocephalosyndactyly type 1
Argininosuccinate lyase deficiency ASL deficiency
Arteriohepatic dysplasia  
ASL deficiency  
Aspartylglucosaminuria AGU
AT  
Ataxia telangiectasia AT, Louis–Bar syndrome
Autoimmune lymphoproliferative syndrome ALPS, Canale-Smith syndrome
Axenfeld anomaly  
Axenfeld-Rieger syndrome Axenfeld anomaly, Rieger anomaly
Becker myotonia  
Behçet disease --
Benign essential blepharospasm  
Best vitelliform macular dystrophy --
Bladder exstrophy --
Blepharospasm Benign essential blepharospasm
Bourneville disease  
Brain disease of unknown cause  
Bruton disease/agammaglobulinemia  
Bullous ichthyosis  
CADASIL Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy
Canale-Smith syndrome  
Cardiofaciocutaneous syndrome CFC
CATCH 22  
CCHS  
Central core disease --
Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy  
Cerebral gigantism  
CF  
Childhood disintegrative disorder Heller syndrome
Chondroectodermal dysplasia  
Christ-Siemens-Touraine syndrome  
Chromosome 1, 1p36 deletion syndrome  
Chromosome 1, Monosomy 1p36  
Chromosome 13, 13q deletion syndrome  
Chromosome 13, Monosomy 13q syndrome  
Chromosome 20, Monosomy 20p12 syndrome  
Chromosome 22, 22q11 deletion syndrome  
Chromosome 22, CATCH 22  
Chromosome 5, 5p deletion syndrome  
Chronic inflammatory demyelinating polyneuropathy  
Churg-Strauss syndrome --
CIDP Chronic inflammatory demyelinating polyneuropathy
Cockayne syndrome --
Comel-Netherton syndrome  
Common variable immunodeficiency CVID, Variable immunodeficiency, Hypogammaglobulinemia
Congenital bilateral perisylvian syndrome  
Congenital brittle bone disease  
Congenital central hypoventilation syndrome CCHS
Congenital dystrophia myotonica  
Congenital myasthenia --
Congenital myotonia Myotonia congenita, Thomsen disease, Becker myotonia
Congenital spondyloepiphyseal dysplasia Spondyloepiphyseal dysplasia congenita
Costello syndrome Faciocutaneoskeletal syndrome, FCS syndrome
Cri du chat syndrome 5p deletion syndrome
CVID  
Cystic fibrosis CF, Pancreatic cystic fibrosis, Muscoviscidosis
Cystinosis --
Danon disease Lysosomal-associated membrane protein 2, LAMP2
Darier disease Keratosis follicularis
De Morsier syndrome  
Dermatomyositis --
DiGeorge syndrome  
Dyskeratosis congenita Hoyeraal-Hreidarsson syndrome
Dystrophia myotonica type 1  
Dystrophia myotonica type 2  
Early-onset retinitis pigmentosa  
Ectodermal dysplasia  
Ellis-van Creveld syndrome and Weyers acrofacial dysostosis Chondroectodermal dysplasia
Erythropoietic protoporphyria Porphyria, erythropoietic protoporphyria
Eulenburg disease  
Fabry disease Anderson-Fabry disease, Alpha-galactosidase A deficiency, Angiokeratoma corporis diffusum
Faciocutaneoskeletal syndrome  
Fanconi anaemia --
FCS syndrome  
Floating Harbor syndrome Pelletier-Leisti syndrome
Foix-Chavany-Marie syndrome  
Gillespie syndrome --
Glycogenosis type II  
Glycogenosis type V  
Glycogenosis type VII  
GM2 gangliosidoses Hexosaminidase A deficiency, Tay-Sachs disease, Hexosaminidase B deficiency, Sandhoff disease,...
HAE  
HAE  
Heller syndrome  
Hepatolenticular degeneration  
Hereditary angioedema HAE
Hexosaminidase A deficiency  
Hexosaminidase B deficiency  
HIES  
Hoyeraal-Hreidarssons syndrome  
Huntington chorea  
Huntington disease HD, Huntington chorea, Juvenile Huntington disease
Hyper IgE syndrome Job disease, Hyperimmunoglobulin E syndrome, HIES
Hyperimmunoglobulin E syndrome  
Hyperkalemic periodic paralysis and Paramyotonia congenita HyperPP, Eulenburg disease
HyperPP  
Hypogammaglobulinemia  
Hypohidrotic ectodermal dysplasia Anhidrotic ectodermal dysplasia, Ectodermal dysplasia, Christ-Siemens-Touraine syndrome
Ichthyosis Bullous ichthyosis, Lamellar ichthyosis
Immunodysregulation, polyendocrinopathy, and enteropathy, X-linked  
IPEX syndrome Immunodysregulation, polyendocrinopathy, and enteropathy, X-linked; IPEX-like syndrom
IPEX-like syndrome  
Isaacs syndrome --
Job disease  
Juvenile Huntington disease  
Kabuki makeup syndrome  
Kabuki syndrome Kabuki makeup syndrome, Niikawa-Kuroki syndrome
Kennedy disease Spinal bulbar muscular atrophy, SBMA
Keratosis follicularis  
Klippel-Trenaunay syndrome Klippel-Trenaunay-Weber syndrome, Angioosteohypertrophy syndrome
Klippel-Trenaunay-Weber syndrome  
Kostmann disease  
Lamellar ichthyosis  
LAMP2  
Landau-Kleffner syndrome Acquired epilectic aphasia
Langer-Giedion syndrome  
Late-onset spondyloepiphyseal dysplasia Spondyloepiphyseal dysplasia tarda
LCA  
LCHAD deficiency Long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency
Leber congenital amaurosis LCA, Early-onset retinitis pigmentosa
Long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency  
Louis-Bar syndrome  
LPI  
Lysinuric protein intolerance LPI
Lysosomal-associated membrane protein 2  
Malignant hyperthermia --
Maple syrup urine disease MSUD
Marble bone disease  
McArdle disease Glycogenosis type V, Myophosphorylase deficiency
McCune-Albright syndrome --
MED  
Microcephaly vera  
Moebius syndrome  
Mohr syndrome (OFD II)  
Monosomy 13q syndrome  
Monosomy 1p36  
Motor neurone disease  
MSUD  
Multiple epiphyseal dysplasia MED
Muscle glycogen storage disease type VII  
Muscle phosphofructokinase deficiency  
Muscoviscidosis  
Myophosphorylase deficiency  
Myotonia congenita  
Myotonic dystrophy Steinert disease, Dystrophia myotonica type 1, Congenital dystrophia myotonica, Dystrophia...
Möbius sequence  
Möbius syndrome Moebius syndrome, Möbius sequence
Nemaline myopathy --
Netherton syndrome Comel-Netherton syndrome
Neuromyotonia  
Niikawa-Kuroki syndrome  
Noonan syndrome --
OFD I and II  
OI  
ONH syndrome  
Opercular syndrome  
Optic nerve hypoplasia ONH syndrome, Septo-optic dysplasia, De Morsier syndrome
Oral-facial-digital syndrome I and II OFD I and II, Papillon-Léage-Psaume syndrome (OFD I), Mohr syndrome (OFD II)
Osteogenesis imperfecta OI, Congenital brittle bone disease
Osteopetrosis Albers-Schönberg disease, Marble bone disease
Pachyonychia congenita PC
PAN  
Pancreatic cystic fibrosis  
Papillon-Léage-Psaume syndrome (OFD I)  
Paramyotonia congenita  
Paroxysmal nocturnal haemoglobinuria PNH
PC  
Pelizaeus-Merzbacher disease PMD
Pelletier-Leisti syndrome  
Perisylvian syndrome Congenital bilateral perisylvian syndrome, Opercular syndrome, Foix-Chavany-Marie syndrome,...
Phenylketonuria PKU
Phosphofructokinase deficiency  
PKU  
PMD  
PNH  
Polyarteritis nodosa PAN
Polymyositis --
Pompe disease Glycogenosis type II, Acid maltase deficiency
Porphyria, acute intermittent porphyria  
Porphyria, erythropoietic protoporphyria  
Prader-Willi syndrome PWS
Primary lateral sclerosis  
Primary microcephaly Microcephaly vera
Progressive bulbar palsy  
Progressive spinal muscular atrophy  
PROMM  
Proximal myotonic myopathy,  
Pseudoachondroplasia --
Pseudobulbar palsy  
PWS  
Retinoblastoma --
Rett syndrome --
Rieger anomaly  
Rubinstein-Taybi syndrome --
Russell-Silver syndrome  
Sandhoff disease  
SBMA  
SCID  
SCN  
SDS  
Septo-optic dysplasia  
Severe combined immunodeficiency SCID
Severe congenital neutropenia SCN, Kostmann disease
Sex-linked agammaglobulinemia  
Sex-linked gammaglobulin deficiency  
Shwachman Diamond syndrome  
Shwachman syndrome Shwachman-Diamond syndrome, SDS
Sickle cell anaemia --
Silver-Russell syndrome Russell-Silver syndrome
SLO syndrome  
SLOS  
Smith-Lemli-Opitz syndrome SLOS, SLO syndrome
Sotos syndrome Cerebral gigantism
Spinal bulbar muscular atrophy  
Spondyloepiphyseal dysplasia congenita  
Spondyloepiphyseal dysplasia tarda  
SSADH deficiency  
Steinert disease  
Succinic semialdehyde dehydrogenase deficiency SSADH deficiency
Takayasu arteritis --
TAR syndrome --
Tarui disease Glycogenosis type VII, Phosphofructokinase deficiency, Muscle glycogen storage disease type VII,...
Tay-Sachs disease  
Testicular feminisation syndrome  
Thalassemia --
Thomsen disease  
Trichorhinophalangeal syndrome TRPS, Langer-Giedion syndrome
TRPS  
TSC  
Tuberous sclerosis Tuberous sclerosis complex, TSC, Bourneville disease
Tuberous sclerosis complex  
Tyrosinemia type 1 --
Usher syndrome --
WAGR  
WAGR syndrome Wilms tumour, aniridia, genital abnormalities and retardation; WAGR
Variable immunodeficiency  
Warts, hypogammaglobulinemia, infections, and myelokathexis  
Velo-cardio-facial syndrome  
Weyers acrofacial dysostosis  
WHIM syndrome Warts, hypogammaglobulinemia, infections, and myelokathexis, Zuelzer-Krills syndrome
Williams syndrome Williams-Beuren syndrome
Williams-Beuren syndrome  
Wilms tumour, aniridia, genital abnormalities and retardation  
Wilson disease Hepatolenticular degeneration
Wiskott-Aldrich syndrome --
Worster-Drought syndrome  
X-linked agammaglobulinemia Bruton disease/agammaglobulinemia, Sex-linked gammaglobulin deficiency, Sex-linked...
Zuelzer-Krills syndrome